Background: Ectopic spleen is a rare condition in which the spleen is not in its original location. Simultaneous occurrence of thrombocytopenia, enlarged spleen (splenomegaly) and ectopic spleen is very rare.

Case Report: A 19 year- old married woman referred to Tohid Hospital with symptoms of pain, pressure and heaviness in the right upper quadrant (RUQ). On physical examination, a mass with firm consistency and a smooth wall in the right side of the abdomen around the navel, was palpated. Further investigations revealed, thrombocytopenia (Plt = 70000) and a large homogeneous mass with well defined wall, in the right upper quadrant (RUQ), in the anatomic site of left liver lobe. One week after splenectomy, platelet count increased to 250,000, and the symptoms disappeared.

Conclusion: Diagnosis of ectopic spleen or wandering spleen was considered for this patient. We found simultaneous occurrence of thrombocytopenia, splenomegaly and ectopic spleen in our patient which is a very rare condition.

Keywords: Ectopic spleen, Thrombocytopenia, Abdominal mass.

Received: Apr 11, 2016      Accepted: Sep 5, 2016